Page 97 - The Vasculitides, Volume 1: General Considerations and Systemic Vasculitis
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Epidemiology of Primary Systemic Vasculitis                 73

210.5 per 100,000 exceeded the mean Asian and Pacific children annual incidence of 62.9 per
100,000 children, followed by native Hawaiian children with an incidence of 86.9, other
Asian children with an incidence of 84.9, and Chinese children with an incidence of 83.2 per
100,000 exceeding that of whites with an incidence of KD of 13.7 per 100,000 children.

                        Table 5. Global Incidence and Prevalence of KD

Authors (References)    Country      Study Period  Incidence per        Prevalence
                                                   106                  per 106

                        Australia    1990-1999     7.96 per 106         --

Saundankar et al. [73]  Australia    2000-2009     9.34                 --

                        Australia    2005          15.7                 --

                        Canada1      1995-2006     26.22                --

Lin et al. [74]         Canada1      1995-2006     6.83                 --
                        Canada1      1995          14.394               --

                        Canada1      2006          26.244               --

                        China5       2003-2007     46.322               --

Ma et al. [75]          China5       2003          36.782               --

                        China5       2007          53.282               --

                        China6       1997-2001     7.062                --

Li et al. [76]          China6       1997          8.572                --

                        China6       2001          9.812                --

                        China7       2000-2004     49.42                --

Du et al. [77]          China7       2000          40.92                --

                        China7       2004          55.12                --

Fischer et al. [78]     Denmark      1981-2004     4.5-5.0              --

Holman et al. [79]      Hawaii       1996-2006     50.4                 --

Ng et al. [81]          Hong Kong    1994-1997     26.0                 --
                        Hong Kong    1994-1997     39.0                 --

Singh et al. [81]       North India  1994          0.51                 --
                        North India  2007          4.5                  --

Nakamura et al. [82]    Japan        2009          206.2                --
                        Japan        2010          239.6                --

                        Korea        2006-2008     113.1                --

Park et al. [83]        Korea        2006          108.7                --

                        Korea        2008          113.1                --

Schiller et al. [84]    Sweden       1990-1992     2.9                  --
                        Sweden       1990-1992     6.22                 --

Lue et al. [85]         Taiwan       2006          66.242               --

Huang et al. [86]       Taiwan       2003-2006     153.0                --
                        Taiwan       2003-2006     69.02                --

Harnden et al. [87]     UK           1991 4.8 --
                        UK           2000 9.2 --

Holman et al. [88]      US           2006          20.8                 --

1Ontario; 2age <5 years; 3age 5 to 9 years; 4age 10 to 14 years; 5Shanghai; 6Sichuan Provence; 7Beijing.

Ng and colleagues [80] conducted retrospective and prospective studies of KD in Hong Kong
respectively between 1994 to 1997 and from 1997 to 2000 identifying 696 children < 15 years
of age and noting a higher incidence of KD in the prospective period (39 versus 26 per

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